Please use this identifier to cite or link to this item:
http://acervodigital.unesp.br/handle/11449/13189
Full metadata record
DC Field | Value | Language |
---|---|---|
dc.contributor.author | Sato, Juliana de Oliveira | - |
dc.contributor.author | Sallum, A. M. E. | - |
dc.contributor.author | Ferriani, V. P. L. | - |
dc.contributor.author | Marini, R. | - |
dc.contributor.author | Sacchetti, S. B. | - |
dc.contributor.author | Okuda, E. M. | - |
dc.contributor.author | Carvalho, J. F. | - |
dc.contributor.author | Pereira, R. M. R. | - |
dc.contributor.author | Len, C. A. | - |
dc.contributor.author | Terreri, M. T. | - |
dc.contributor.author | Lotufo, S. A. | - |
dc.contributor.author | Romanelli, P. R. | - |
dc.contributor.author | Ramos, V. C. S. | - |
dc.contributor.author | Hilario, M. O. | - |
dc.contributor.author | Silva, C. A. | - |
dc.contributor.author | Corrente, José Eduardo | - |
dc.contributor.author | Saad-Magalhaes, C. | - |
dc.date.accessioned | 2014-05-20T13:38:02Z | - |
dc.date.accessioned | 2016-10-25T16:54:26Z | - |
dc.date.available | 2014-05-20T13:38:02Z | - |
dc.date.available | 2016-10-25T16:54:26Z | - |
dc.date.issued | 2009-11-01 | - |
dc.identifier | http://www.ncbi.nlm.nih.gov/pubmed/20149327 | - |
dc.identifier.citation | Clinical and Experimental Rheumatology. Pisa: Clinical & Exper Rheumatology, v. 27, n. 6, p. 1031-1038, 2009. | - |
dc.identifier.issn | 0392-856X | - |
dc.identifier.uri | http://hdl.handle.net/11449/13189 | - |
dc.identifier.uri | http://acervodigital.unesp.br/handle/11449/13189 | - |
dc.description.abstract | ObjectiveTo describe onset features, classification and treatment of juvenile dermatomyositis (JDM) and juvenile polymyositis (JPM) from a multicentre registry.MethodsInclusion criteria were onset age lower than 18 years and a diagnosis of any idiopathic inflammatory myopathy (IIM) by attending physician. Bohan & Peter (1975) criteria categorisation was established by a scoring algorithm to define JDM and JPM based oil clinical protocol data.ResultsOf the 189 cases included, 178 were classified as JDM, 9 as JPM (19.8: 1) and 2 did not fit the criteria; 6.9% had features of chronic arthritis and connective tissue disease overlap. Diagnosis classification agreement occurred in 66.1%. Medial? onset age was 7 years, median follow-up duration was 3.6 years. Malignancy was described in 2 (1.1%) cases. Muscle weakness occurred in 95.8%; heliotrope rash 83.5%; Gottron plaques 83.1%; 92% had at least one abnormal muscle enzyme result. Muscle biopsy performed in 74.6% was abnormal in 91.5% and electromyogram performed in 39.2% resulted abnormal in 93.2%. Logistic regression analysis was done in 66 cases with all parameters assessed and only aldolase resulted significant, as independent variable for definite JDM (OR=5.4, 95%CI 1.2-24.4, p=0.03). Regarding treatment, 97.9% received steroids; 72% had in addition at least one: methotrexate (75.7%), hydroxychloroquine (64.7%), cyclosporine A (20.6%), IV immunoglobulin (20.6%), azathioprine (10.3%) or cyclophosphamide (9.6%). In this series 24.3% developed calcinosis and mortality rate was 4.2%.ConclusionEvaluation of predefined criteria set for a valid diagnosis indicated aldolase as the most important parameter associated with de, methotrexate combination, was the most indicated treatment. | en |
dc.format.extent | 1031-1038 | - |
dc.language.iso | eng | - |
dc.publisher | Clinical & Exper Rheumatology | - |
dc.source | Web of Science | - |
dc.subject | Idiopathic inflammatory myopathy | en |
dc.subject | juvenile dermatomyositis | en |
dc.subject | juvenile polymyositis | en |
dc.subject | methotrexate | en |
dc.subject | steroids | en |
dc.title | A Brazilian registry of juvenile dermatomyositis: onset features and classification of 189 cases | en |
dc.type | outro | - |
dc.contributor.institution | Universidade Estadual Paulista (UNESP) | - |
dc.contributor.institution | Universidade de São Paulo (USP) | - |
dc.contributor.institution | Universidade Estadual de Campinas (UNICAMP) | - |
dc.contributor.institution | Universidade Federal de São Paulo (UNIFESP) | - |
dc.contributor.institution | Hosp Municipal Infantil Menino Jesus | - |
dc.contributor.institution | Pontifícia Universidade Católica de São Paulo (PUC-SP) | - |
dc.description.affiliation | Univ Estradual Paulista, UNESP, Dept Paediat, Fac Med Botucatu, BR-18618970 São Paulo, Brazil | - |
dc.description.affiliation | FMUSP, Inst Crianca, São Paulo, Brazil | - |
dc.description.affiliation | Univ São Paulo, Fac Med Ribeirao Preto, São Paulo, Brazil | - |
dc.description.affiliation | Univ Estadual Campinas, UNICAMP, Fac Ciencias Med, BR-13081970 Campinas, SP, Brazil | - |
dc.description.affiliation | Fac Ciencias Med Santa Casa São Paulo, São Paulo, Brazil | - |
dc.description.affiliation | FMUSP, Disciplina Reumatol, São Paulo, Brazil | - |
dc.description.affiliation | Univ Fed São Paulo, Escola Paulista Med, São Paulo, Brazil | - |
dc.description.affiliation | Hosp Municipal Infantil Menino Jesus, São Paulo, Brazil | - |
dc.description.affiliation | PUC São Paulo, Dept Reumatol, São Paulo, Brazil | - |
dc.description.affiliationUnesp | Univ Estradual Paulista, UNESP, Dept Paediat, Fac Med Botucatu, BR-18618970 São Paulo, Brazil | - |
dc.identifier.wos | WOS:000274264700026 | - |
dc.rights.accessRights | Acesso restrito | - |
dc.relation.ispartof | Clinical and Experimental Rheumatology | - |
dc.identifier.orcid | 0000-0001-5478-4996 | pt |
Appears in Collections: | Artigos, TCCs, Teses e Dissertações da Unesp |
There are no files associated with this item.
Items in DSpace are protected by copyright, with all rights reserved, unless otherwise indicated.